Chapter 21

    Both arteries, aorta and pulmonary, arise from the right ventricle. Almost always is associated with VSD.
    Probably the majority of cases occur with pulmonary stenosis and VSD, behaving as a severely cyanotic Tetralogy of Fallot.
    Three Principal Varieties Can Be Recognized:

Type I:	With VSD, but not pulmonary stenosis. The VSD is located below the crista supraventricularis. The patient has minimal cyanosis and repetitive bronchitis.
Type II:	With VSD, located above the crista supraventricularis and no pulmonary stenosis. Severe cyanosis of early appearance (many times appearing during the first month of life).
Type III:	With VSD and pulmonary stenosis. Early cyanosis. Looks like severe Tetralogy of Fallot.

Type II double outlet right ventricle, with ventricular septal defect located above the crista supraventricularis. This type of defect usually produces a clinical picture which is very similar to the one of ventricular septal defect with cyanosis which appears early in life.

Type III double outlet right ventricle with large ventricular septal defect and subvalvular pulmonary stenosis.

Diagrammatic representation of Double Outlet Right Ventricle. VSD can be located above or below the Crista Supraventricularis as shown in the diagram.